| Item Type | Name |
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Concept
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Age Factors
|
|
Concept
|
Amyotrophic Lateral Sclerosis
|
|
Concept
|
Arcuate Nucleus of Hypothalamus
|
|
Concept
|
Blood Pressure
|
|
Concept
|
Amino Acid Sequence
|
|
Concept
|
Animals, Newborn
|
|
Concept
|
Computer Simulation
|
|
Concept
|
Base Sequence
|
|
Concept
|
beta-Endorphin
|
|
Concept
|
Biopsy
|
|
Concept
|
Epilepsy, Temporal Lobe
|
|
Concept
|
Bradycardia
|
|
Concept
|
Brain Stem
|
|
Concept
|
Chromosomes, Human, Pair 3
|
|
Concept
|
Cerebellum
|
|
Concept
|
Cerebral Ventricles
|
|
Concept
|
Inclusion Bodies
|
|
Concept
|
Cytosol
|
|
Concept
|
Dementia
|
|
Concept
|
Catecholamines
|
|
Concept
|
Freeze Drying
|
|
Concept
|
Endoplasmic Reticulum
|
|
Concept
|
Endorphins
|
|
Concept
|
Image Enhancement
|
|
Concept
|
Chromosomes, Human, Pair 17
|
|
Concept
|
Disease Susceptibility
|
|
Concept
|
Drug Evaluation, Preclinical
|
|
Concept
|
Hippocampus
|
|
Concept
|
Histological Techniques
|
|
Concept
|
Electroencephalography
|
|
Concept
|
Enkephalin, Leucine
|
|
Concept
|
Genetic Carrier Screening
|
|
Concept
|
Flow Cytometry
|
|
Concept
|
Fluorescent Antibody Technique
|
|
Concept
|
Lyme Disease
|
|
Concept
|
Kuru
|
|
Concept
|
Iatrogenic Disease
|
|
Concept
|
Naltrexone
|
|
Concept
|
Immunohistochemistry
|
|
Concept
|
Injections, Intraventricular
|
|
Concept
|
Ophthalmoplegia
|
|
Concept
|
Molecular Sequence Data
|
|
Concept
|
Cricetinae
|
|
Concept
|
Libya
|
|
Concept
|
Peptide Hydrolases
|
|
Concept
|
Endopeptidases
|
|
Concept
|
Naloxone
|
|
Concept
|
Risk Factors
|
|
Concept
|
Tryptamines
|
|
Concept
|
Receptors, Adrenergic, alpha
|
|
Concept
|
Creutzfeldt-Jakob Syndrome
|
|
Concept
|
Incidence
|
|
Concept
|
Gerstmann-Straussler-Scheinker Disease
|
|
Concept
|
Injections, Intravenous
|
|
Concept
|
Intracellular Membranes
|
|
Concept
|
Hematopoietic Stem Cell Transplantation
|
|
Concept
|
Aphasia, Primary Progressive
|
|
Concept
|
Central Nervous System Neoplasms
|
|
Concept
|
Prevalence
|
|
Concept
|
Gene Expression
|
|
Concept
|
Case-Control Studies
|
|
Concept
|
tau Proteins
|
|
Concept
|
Disease Progression
|
|
Concept
|
Transgenes
|
|
Concept
|
Parkinson Disease
|
|
Concept
|
Parahippocampal Gyrus
|
|
Concept
|
Fatal Outcome
|
|
Concept
|
Endopeptidase K
|
|
Concept
|
Insomnia, Fatal Familial
|
|
Concept
|
Wasting Disease, Chronic
|
|
Concept
|
Benzodioxoles
|
|
Concept
|
Cognitive Dysfunction
|
|
Concept
|
Blotting, Western
|
|
Concept
|
Life Tables
|
|
Concept
|
Prion Diseases
|
|
Concept
|
Codon, Nonsense
|
|
Concept
|
Amyloid beta-Peptides
|
|
Concept
|
Repetitive Sequences, Amino Acid
|
|
Concept
|
Two-Hybrid System Techniques
|
|
Concept
|
Cell Line, Tumor
|
|
Concept
|
Alzheimer Disease
|
|
Concept
|
Coronary Artery Bypass
|
|
Concept
|
Disease Models, Animal
|
|
Concept
|
Fasciculation
|
|
Concept
|
Genetic Counseling
|
|
Concept
|
Genetic Testing
|
|
Concept
|
Hypothalamus
|
|
Concept
|
Mesocricetus
|
|
Concept
|
Protons
|
|
Concept
|
Thalamus
|
|
Concept
|
Neurofibrillary Tangles
|
|
Concept
|
Age of Onset
|
|
Concept
|
Genetic Predisposition to Disease
|
|
Concept
|
Fluorescence Resonance Energy Transfer
|
|
Academic Article
|
Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease.
|
|
Academic Article
|
Prion protein conformation in a patient with sporadic fatal insomnia.
|
|
Academic Article
|
Changes of hippocampal N-acetyl aspartate and volume in Alzheimer's disease. A proton MR spectroscopic imaging and MRI study.
|
|
Academic Article
|
A transmembrane form of the prion protein in neurodegenerative disease.
|
|
Academic Article
|
Amyotrophy in prion diseases.
|
|
Academic Article
|
The prion diseases.
|
|
Academic Article
|
Inherited prion disease caused by the V210I mutation: transmission to transgenic mice.
|
|
Academic Article
|
Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene.
|
|
Academic Article
|
"Out, damned spot! out, I say!...": issues related to prion decontamination.
|
|
Academic Article
|
The charge structure of helix 1 in the prion protein regulates conversion to pathogenic PrPSc.
|
|
Academic Article
|
The AGAAAAGA palindrome in PrP is required to generate a productive PrPSc-PrPC complex that leads to prion propagation.
|
|
Academic Article
|
A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP.
|
|
Academic Article
|
Activation of central mu-opioid receptors is involved in clonidine analgesia in rats.
|
|
Academic Article
|
Prion protein codon 129 genotype prevalence is altered in primary progressive aphasia.
|
|
Academic Article
|
Activation of brainstem endorphinergic neurons causes cardiovascular depression and facilitates baroreflex bradycardia.
|
|
Academic Article
|
On the relationship between clonidine hypotension and brain beta-endorphin in the spontaneously hypertensive rat: studies with alpha adrenergic and opiate blockers.
|
|
Academic Article
|
Live cell fluorescence resonance energy transfer predicts an altered molecular association of heterologous PrPSc with PrPC.
|
|
Academic Article
|
Familial prion disease with Alzheimer disease-like tau pathology and clinical phenotype.
|
|
Academic Article
|
Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein.
|
|
Academic Article
|
The prion diseases.
|
|
Academic Article
|
Isolated fascicular abducens nerve palsy and Lyme disease.
|
|
Academic Article
|
Prion disease (PrP-A117V) presenting with ataxia instead of dementia.
|
|
Academic Article
|
Identifying key components of the PrPC-PrPSc replicative interface.
|
|
Academic Article
|
Rapamycin delays disease onset and prevents PrP plaque deposition in a mouse model of Gerstmann-Sträussler-Scheinker disease.
|
|
Academic Article
|
Wrinkles and folds of the prion protein.
|
|
Academic Article
|
Cytosolic prion protein toxicity is independent of cellular prion protein expression and prion propagation.
|
|
Academic Article
|
A novel human disease with abnormal prion protein sensitive to protease.
|
|
Academic Article
|
Generation of a new form of human PrP(Sc) in vitro by interspecies transmission from cervid prions.
|
|
Academic Article
|
Tunicamycin produces TDP-43 cytoplasmic inclusions in cultured brain organotypic slices.
|
|
Academic Article
|
A cryostat-freeze drying technique for enhanced visualization of catecholamine/indoleamine-containing neurons.
|
|
Academic Article
|
Systemic transthyretin amyloidosis in a patient with bent spine syndrome.
|
|
Academic Article
|
In vivo parahippocampal white matter pathology as a biomarker of disease progression to Alzheimer's disease.
|
|
Academic Article
|
Early Delivery of Misfolded PrP from ER to Lysosomes by Autophagy.
|
|
Academic Article
|
Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition).
|
|
Academic Article
|
Acute encephalopathy as the initial manifestation of CADASIL.
|
|
Academic Article
|
IVIG Delays Onset in a Mouse Model of Gerstmann-Sträussler-Scheinker Disease.
|
|
Academic Article
|
Impaired transmissibility of atypical prions from genetic CJDG114V.
|
|
Academic Article
|
Anle138b prevents PrP plaque accumulation in Tg(PrP-A116V) mice but does not mitigate clinical disease.
|
|
Academic Article
|
"Dual Disease" TgAD/GSS mice exhibit enhanced Alzheimer's disease pathology and reveal PrPC-dependent secretion of Aß.
|
|
Academic Article
|
A novel PRNP-G131R variant associated with familial prion disease.
|
|
Academic Article
|
An atypical presentation of primary central nervous system lymphoma: A case report.
|
|
Academic Article
|
Generation of human chronic wasting disease in transgenic mice.
|
|
Academic Article
|
A Novel TBK1 Variant (Lys694del) Presenting With Corticobasal Syndrome in a Family With FTD-ALS Spectrum Diseases: Case Report.
|
|
Academic Article
|
Challenging Cases of Neurocognitive Disorders.
|
|
Academic Article
|
A case report of a patient with primary familial brain calcification with a PDGFRB genetic variant.
|